Skeleton_Key

应用科学类纪录片，BBC 频道 1999 年出品，是 BBC Horizon 系列其中之一。

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影片信息

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影片原始规格:

• 中文片名 ：

• 中文系列名：BBC 地平线

• 英文片名 ：Skeleton Key

• 英文系列名：BBC Horizon

• 电视台 ：BBC

• 地区 ：英国

• 语言 ：英语

• 时长 ：约 48 分钟

• 版本 ：TV

• 发行时间 ：1999

影片内容介绍

剧情简介

The rare disease known as Fibrodysplasia Ossificans Progressiva (FOP) is featured in this edition of Horizon, the long running flagship BBC science documentary series.

FOP can cause terrible disability, and causes the muscle and ligaments of sufferers to turn into solid bone.

Many FOP patients are children or teenagers.

Any injury to muscle or connective tissue can kick-start a flare up of the condition during which the body produces a new piece of bone around the damaged site. The bone that is formed can grow, repair itself and even harbour marrow in the same way that normal bones do. The new bone rapidly becomes permanent, and can eventually join up with the normal skeleton, leading to devastating mobility problems.

Sufferers can end up fused in a standing poisition, so rigid that they must sleep leaning in a corner. They may eventually die from starvation, when their jaw fuses shut, or suffocate as new bone crushes their lungs.

Scientists have been striving for 15 years to try to understand and cure the condition which affects one in two million people.

Horizon investigates this pioneering research, and the hope it gives to FOP patients.